DEVERGIE’S DISEASE – CLINICAL CASE
DOI:
https://doi.org/10.52340/jecm.2025.06.27Keywords:
Pityriasis rubra pilaris, Devergie’s disease, Follicular hyperkeratosis, CARD14 mutationAbstract
Devergie’s disease (pityriasis rubra pilaris – PRP) is an idiopathic inflammatory, papulosquamous dermatosis. Clinically, it is characterized by disordered keratinization and the formation of hyperkeratotic follicular papules that coalesce into the orange-red plaques, between these areas the skin is not changed “islands of sparing” - are observed. Possible associations include infectious diseases, autoimmune processes, medication-induced reactions, and malignant neoplasms.
The article describes a clinical case of Devergie’s disease. Patient S.E., 56 years old. 26.04.25, “Kani Clinic.” The patient complained of a generalized skin rash. General condition: satisfactory. On the trunk, upper, and lower extremities, numerous, separately distributed, orange-colored hyperkeratotic follicular papules were noted. On the extensor surface of the upper extremity, a solitary plaque was present.
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