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Abstract
Malignant peripheral nerve sheet tumors (MPNST) are uncommon and rare condition. These neoplasms are often associated with neurofibromatosis type I (NF-I) but can also occur sporadically. This article presents a rare case report discussing the detailed diagnostic approach along with an extensive review of the literature for malignant peripheral nerve sheath tumor arising in the left gluteus. A 16 years old boy presented with a large tumor in left gluteus. The patient noticed mass in the left gluteus several years earlier. Patient was complaining about a growing lump tissue under the skin, pain, loss of control of muscles in left leg. Biopsy of the left gluteus showed malignant neoplasm and malignant nerve sheet tumor components were predominant. Surgery was performed with total resection. The operation was performed under general anesthesia. An elliptical incision was made on the tumor and the pathological center was found and released from the surrounding tissues. Pathological blood vessels were clamped and cut. A detailed revision was made and the tumor was removed within healthy tissues. Tumor size was 20X25X20-cm. The patient underwent rehabilitation successfully. No recurrence has been observed in the last 4 years.
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