Abstract
Synovial sarcoma (SS) of kidney (especially the bipha- sic subtype) is a very rare disease, with aggressive behavior, poor prognosis and difficult to diagnose. Here, we present a case of a 32-year-old female, clinically diagnosed as renal cell carcinoma. Right nephrectomy specimen showed a cystic tumor in the upper pole of kidney with areas of hemorrhage and solid growth. Histologically seen morphologic and immunohistochemical features were compatible with the diagnosis of biphasic subtype of SS of kidney. Vimentin and Bcl 2 positivity can be regarded as specific diagnostic markers, but for the final confirmation of the diagnosis, it is desirable to carry out fluorescent in situ hybridization (FISH) or reverse transcriptase polymerase chain reaction (RT-PCR) methods. The presented case is interesting because of its rarity.
References
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