Abstract
Ollier’s Disease (Enchondromatosis) is a rare, non-hereditary osteochondrodysplasia characterized by multiple exostoses. This condition is often accompanied by skeletal deformities, limb asymmetry, functional limitations and chronic pain. In progressive cases, surgical intervention is frequently required, particularly in pediatric patients, where bone growth is in an active phase.
An 11-year-old male patient was admitted to the clinic with genu valga and plano-valgus deformity of the right lower limb, which had been progressing over the years. Multiple exostoses were noted in the knee and ankle joints, with a 3 cm shortening of the right lower limb and marked limping associated with severe pain. The patient had previously undergone unsuccessful surgical intervention.
Instrumental investigations revealed medial epiphysiodesis of the right tibia using a screw and an osteocartilaginous exostosis localized in the distal part of the right fibula. Based on clinical and radiological findings, Ollier’s disease was diagnosed and repeat surgical intervention was planned.
The operation was performed using an open technique. A partial resection of the distal third of the right fibula was conducted with preservation of the syndesmosis. Corrective arcuate osteotomy of the right tibia was performed and three Kirschner wires were used for bone stabilization, aiming to correct the deformity and improve joint mobility. Simultaneously, femoral epiphysiodesis was carried out to balance limb growth rates and achieve symmetry.
Management of Ollier’s disease requires an individualized approach, particularly in pediatric patients where bone growth and deformity progression are anticipated. This clinical case demonstrates that the effectiveness of surgical treatment depends on timely diagnosis and postoperative monitoring. The use of internal fixation plays a crucial role in bone stabilization and healing. Ongoing dynamic observation is necessary to prevent potential complications in the future.
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